Tetralogy of Fallot
The adult after Fallot repair, with pulmonary regurgitation and RV dilatation, when to replace the pulmonary valve, QRS duration and sudden death, and 22q11.2 deletion.
Tier 2Condition
Written with AI assistance and fact-checked against the sources below. For exam study, not clinical decisions. How notes are made
At a glance
- The commonest cyanotic congenital heart disease, about 1 in 2,500 to 3,000 births.
- Four parts: VSD, overriding aorta, RVOT obstruction and RV hypertrophy. The RVOT obstruction sets the degree of right-to-left shunting.
- Almost every adult in Australia has had complete repair in infancy. Unrepaired adults are rare and mostly migrants.
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Sources
- Nicolae M, Gentles T, Strange G et al. Adult congenital heart disease in Australia and New Zealand: a call for optimal care. Heart Lung Circ 2019;28(4):521-529. doi:10.1016/j.hlc.2018.10.015AU/NZCardiac Society of Australia and New Zealand (Paediatric and Congenital Council), 2019
- 2025 ACC/AHA/HRS/ISACHD/SCAI Guideline for the Management of Adults With Congenital Heart Disease. J Am Coll Cardiol 2026;87(7):822-976. doi:10.1016/j.jacc.2025.09.006American College of Cardiology and American Heart Association, 2025 (published February 2026)
- Baumgartner H, De Backer J, Babu-Narayan SV et al. 2020 ESC Guidelines for the management of adult congenital heart disease. Eur Heart J 2021;42:563-645. doi:10.1093/eurheartj/ehaa554European Society of Cardiology, 2020
- De Backer J, Haugaa KH, Hasselberg NE et al. 2025 ESC Guidelines for the management of cardiovascular disease and pregnancy. Eur Heart J 2025;46(43):4462-4568. doi:10.1093/eurheartj/ehaf193European Society of Cardiology, 2025
- Gatzoulis MA, Balaji S, Webber SA et al. Risk factors for arrhythmia and sudden cardiac death late after repair of tetralogy of Fallot: a multicentre study. Lancet 2000;356:975-81The Lancet, 2000
- Last updated
- 14 November 2026
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